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1 <br />1 Enzyme or protein locus <br />1 <br />1 <br /> <br /> <br />1 <br />n <br />1 <br />1 <br />1 <br /> <br /> <br />t <br />H <br />1 <br /> <br /> <br />18 <br />Enzyme Gene or protein <br />number (E. C.) Buffer symbol <br />Glucose-6-phosphate isomerase-2 5.3.1.9 TEB GPI-2 <br />Glutathione reductase 1.6.4.2 TEB GR <br />Guanylate kinase-1 2.7.4.8 TEB GUK-1 <br />Guanylate kinase-2 2.7.4.8 TC GUK-2 <br />Guanylate kinase-3 2.7.4.8 TEB GUK-3 <br />beta-Glucuronidase 3.2.1.31 TEB BGUS <br />Isocitrate dehydrogenase (NADP+), cytosolic 1.1.1.42 TEB sIDHP <br />Isocitrate dehydrogenase (NADP+), mitochondrial 1.1.1.42 TEB MIDHP <br />L-Lactate dehydrogenase-A 1.1.1.27 TC LDH-A <br />L-Lactate dehydrogenase-B 1.1.1.27 TC LDH-B <br />L-Lactate dehydrogenase-C 1.1.1.27 TC/TEBLDH-C <br />Lactoylglutathione lyase 4.4.1.5 TEB LGL <br />alpha-Mannosidase 3.2.1.24 TEB aMAN <br />Malate dehydrogenase-1, cytosolic 1.1.1.37 TEB sMDH-1 <br />Malate dehydrogenase-2, cytosolic 1.1.1.37 TEB sMDH-2 <br />Malate dehydrogenase, mitochondrial 1.1.1.37 TC mMDH <br />Malic enzyme (NADP+) 1.1.1.40 TEB MEP- I <br />Malic enzyme (NADP+) 1.1.1.40 TC MEP-2 <br />Mannose-6-phosphate isomerase 5.3.1.8 TEB MPI <br />Nucleoside-phosphate kinase 2.7.4.4 TEB NPK <br />Nucleoside-tfiphosphate pyrophosphatase 3.6.1.19 TEB NTP <br />Dipeptidase 3.4.-.- TC PEPA <br />Peptidase-S 3.4.-.- TEB PEPS <br />Tiipeptide aininopeptidase 3.4.11 TEB PEPB <br />Peptidase-C 3.4:: TC PEPC <br />Proline dpeptidase 3.4.13.9 TEB PEPD <br />Phosphoglycerate mutase 5.4.2.1 TEB PGAM-2 <br />Phosphogluconate dehydrogenase-1 1.1.1.44 TEB PGDH-1 <br />Phosphogluconate dehydrogenase-2 1.1.1.44 .TC PGDH-2 <br />Phosphoglycerate kinase 2.7.2.3 TEB PGK <br />Phosphoglucomutase- 1 5.4.2.2 TM PGM-1 <br />Phosphoglucomutase-2 5.4.2.2 TM PGM-2 <br />Pyruvate ki nase- 1 2.7.1.40 TC PK- 1 <br />Pyruvate kinase-2 2.7.1.40 TC PK-2 <br />Pyruvate kinase-3 2.7.1.40 TC PK-3 <br />Purine-nucleoside phosphorylase-1 2.4.2.1 TEB PNP-1 <br />Purine-nucleoside phosphorylase-2 2.4.2.1 TEB PNP-2 <br />Protein-1, muscle TEB PROT-1 <br />Protein-2, muscle TEB PROT-2 <br />Protein-3, muscle TC PROT-3 <br />Protein-4, muscle TC PROT-4 <br />Protein-5, plasma TEB PROT-5 <br />Protein-6, plasma TEB PROT-6 <br />Superoxide dismutase- 1 1.15.1.1 TEB SOD-1 <br />Triose-phosphate isomerase-1 5.3.1.1 RGWY TPI-I <br />Triose-phosphate isomerase-2 5.3.1.1 TEB TPI-2 <br />UDPglucose-hexose- I -phosphate uridylyltransferase 2.7.7.12 TC UGHUT <br />