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07/20/99 10:53 002 <br /> <br />1 <br />r-1 <br />L <br />1 <br /> <br /> <br />1 <br /> <br />1 <br />1 <br />1 <br /> <br /> <br /> <br />1 <br />1 <br /> <br />Enzyme or protein locus <br />17 <br />Enzyme Gene or protein <br />number (E. C.) Buffcr symbol <br />Glucose-6-phosphate isomerase-2 5.3.1.9 TED GPI-2 <br />Glutathione reductasc 1.6.4.2 TBB GR <br />Guanylate kinase-1 2.7.4.8 TEB GUK-1 <br />Guanylate kinase-2 2.7.4.8 TC GUK-2 <br />Guanylate kinase-3 2.7.4.8 TEB GUK-3 <br />beta-Glucuronidase 3.2.1.31 TEB BGUS <br />Isocitrate dehydrogenase (NADP+), cytosolic 1.1.1.42 TED s1DHP <br />Isocitrate dehydrogenase (NA1)PI-), mitochondrial 1.1.1.42 TED MIDHP <br />L-Lactatc dehydrogenase-A 1.1.1.27 TC LDH-A <br />L-Lactate dehydrogenase-B 1.1.1.27 TC LDII-13 <br />I.-Lactate dehydrogenase-C; 1.1.1.27 TC MBLDH-C <br />Lactoylglutathione lyase 4.4.1.5 TED LGL <br />alpha-Mannosidase 3.2.1.24 TED aMAN <br />Malate dehydrogenase-1, cytosoliu 1.1.1.37 TED sMDH-1 <br />Malate dehydrogenase-2, cytosolic 1.1.1.37 TED sMDH-2 <br />Malate dehydrogenase, mitochondrial 1.1.1.37 TC mMDII <br />Malic enzyme (NADP.I) 1.1.1.40 IMB MEP. I <br />Mali; enzyme (NADP+) 1.1.1.40 IV MEP-2 <br />Mannosc-6-phosphato isomerase 5.3.1.8 TED MPI <br />Nucleoside-phosphate kinase 2.7.4.4 TED NPK <br />Nuuleoside-trphosphate pyrophosphatasc 3.6.1.19 TED NTP <br />Dipeptidase 3.4.-.- TC PEPA <br />Peptidase-S 3.4.-.- TED PEPS <br />Tiipeptide aininopeptidase 3.4.11 T13D PEPB <br />Peptidase-C 3.4.-.- TC PEPC <br />Prolinc dipeptidase 3.4.13.9 T13D PEPD <br />Phusphuglycerate mutasc 5.4.2.1 TED PGAM-2 <br />Phosphogluuonate dehydrogenase-1 1.1.1.44 TEB PODII-1 <br />Phohphogluuunate dehydrogenase-2 1.1.1.44 TC PGDII-2 <br />Phosphoglyccrate kinase 2.7.2.3 TED PGK <br />Phosphoglucomutase- 1 5.4.2.2 TM PGM-l <br />Phusphvglucomutase-2 5.4.2.2 TM PGM-2 <br />Pyruvatc ki nase- 1 2.7.1.40 TC PK- 1 <br />Pyruvatc kinase-2 2.7.1.40 TC PK-2 <br />Pyruvatc kinase-3 2.7.1.40 TC PK-3 <br />Purinc-nucleoside phosphorylase-1 2.4.2.1 TED PNP-1 <br />Purine-nucleoside phosphorylase-2 2.4.2.1 TSB PNP-2 <br />Protein-1, muscle TED PROT-1 <br />Protein-2, muscle TER PROT-2 <br />Protein-3, musclc TIC PROT-3 <br />Protein-4, musclc TC PROT-4 <br />Protein-5, plasma TED PROT-5 <br />Protein-6, plasma T13B PROT-6 <br />Superoxide dismutase- 1 1.15.1.1 T113 SOT)-l <br />Triose-phosphate isomerase-1 5.3.1.1 RGWY TPI-I <br />Triose-phosphate isommsc-2 5.3.1.1 TI3D TPI-2 <br />UDPglucose-hexose-l-phosphate uridylyltransfera.se 2.7.7.12 TC UGHUT <br />1